Hereditary Disorders of Dentin: Dentinogenesis Imperfecta Type II and Dentin Dysplasia Type II
نویسندگان
چکیده
منابع مشابه
Hereditary dentine disorders: dentinogenesis imperfecta and dentine dysplasia
The hereditary dentine disorders, dentinogenesis imperfecta (DGI) and dentine dysplasia (DD), comprise a group of autosomal dominant genetic conditions characterised by abnormal dentine structure affecting either the primary or both the primary and secondary dentitions. DGI is reported to have an incidence of 1 in 6,000 to 1 in 8,000, whereas that of DD type 1 is 1 in 100,000. Clinically, the t...
متن کاملDevelopmental Disturbance of Dentin with Probable Diagnosis of Dentin Dysplasia Type 1d: A rare case report
Background: Dentin dysplasia (DD) is a rare disturbance of dentin formation, characterized by normal enamel but atypical dentin formation with abnormal pulpal morphology. In DD type I, the teeth appear clinically normal in morphologic appearance and color. Radiographic analysis shows obliteration of all pulp chambers as well as short, blunted, and malformed or absent roots with multiple periapi...
متن کاملDentin Dysplasia Type I with Hypomature Amelogenesis Imperfecta in an 18-year-old Girl
Introduction: Dentin dysplasia is a rare autosomal dominant inheriting disturbance of dentin formation characterized by normal enamel formation, but atypical dentin with abnormal pulpal morphology. There are two major patterns: type I and type II. Amelogenesis imperfecta is an autosomal dominant. X-link inherent disease that is classified by clinical manifestation into hypoplastic, hyp...
متن کاملDentinogenesis imperfecta type II: an affected family saga.
Dentinogenesis imperfecta (DI) type II or hereditary opalescent dentin is inherited in simple autosomal dominant mode with high penetrance and low mutation rate. It generally affects both the deciduous and permanent dentitions. DI type II corresponds to a localized form of mesodermal dysplasia, observed in histodifferentiation. Early diagnosis and treatment are therefore, fundamental, aiming at...
متن کاملCASE REPORT Dentin dysplasia type I
To cite: Singh A, Gupta S, Yuwanati MB, et al. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/bcr-2013009403 SUMMARY Dentin dysplasia type I is a rare hereditary disturbance of dentin formation characterised clinically by nearly normal appearing crowns and hypermobility of teeth that affects one in every 100 000 individuals and manifests in both primary and permanent...
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ژورنال
عنوان ژورنال: Journal of Operative Dentistry & Endodontics
سال: 2020
ISSN: 2456-320X
DOI: 10.5005/jp-journals-10047-0091